CLPB (caseinolytic peptidase B homolog), the first mitochondrial protein refoldase associated with human disease.

Dagmara Mróz; Hubert Wyszkowski; Tomasz Szablewski; Katarzyna Zawieracz; Rafał Dutkiewicz; Katarzyna Bury; Saskia Wortmann; Ron A Wevers; Szymon Ziętkiewicz

doi:10.1016/j.bbagen.2020.129512

CLPB (caseinolytic peptidase B homolog), the first mitochondrial protein refoldase associated with human disease.

Dagmara Mróz, Hubert Wyszkowski, Tomasz Szablewski, Katarzyna Zawieracz, Rafał Dutkiewicz, Katarzyna Bury, Saskia Wortmann (Co-author), Ron A Wevers, Szymon Ziętkiewicz

Department of Pediatrics

Research output: Contribution to journal › Original Article › peer-review

15 Citations (Web of Science)

Original language	English
Pages (from-to)	129512
Journal	BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS
Volume	1864
Issue number	4
DOIs	https://doi.org/10.1016/j.bbagen.2020.129512
Publication status	Published - 2020

Keywords

3-METHYLGLUTACONIC ACIDURIA
NEUTROPENIA

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10.1016/j.bbagen.2020.129512

Cite this

@article{66d352a3335e47879be3be2306c0268d,

title = "CLPB (caseinolytic peptidase B homolog), the first mitochondrial protein refoldase associated with human disease.",

keywords = "3-METHYLGLUTACONIC ACIDURIA, NEUTROPENIA",

author = "Dagmara Mr{\'o}z and Hubert Wyszkowski and Tomasz Szablewski and Katarzyna Zawieracz and Rafa{\l} Dutkiewicz and Katarzyna Bury and Saskia Wortmann and Wevers, {Ron A} and Szymon Zi{\c e}tkiewicz",

note = "Wortmann: PMU, Univ Childrens Hosp, Salzburg, Austria; ",

year = "2020",

doi = "10.1016/j.bbagen.2020.129512",

language = "English",

volume = "1864",

pages = "129512",

journal = "BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS",

issn = "0304-4165",

number = "4",

}

TY - JOUR

T1 - CLPB (caseinolytic peptidase B homolog), the first mitochondrial protein refoldase associated with human disease.

AU - Mróz, Dagmara

AU - Wyszkowski, Hubert

AU - Szablewski, Tomasz

AU - Zawieracz, Katarzyna

AU - Dutkiewicz, Rafał

AU - Bury, Katarzyna

AU - Wortmann, Saskia

AU - Wevers, Ron A

AU - Ziętkiewicz, Szymon

N1 - Wortmann: PMU, Univ Childrens Hosp, Salzburg, Austria;

PY - 2020

Y1 - 2020

KW - 3-METHYLGLUTACONIC ACIDURIA

KW - NEUTROPENIA

U2 - 10.1016/j.bbagen.2020.129512

DO - 10.1016/j.bbagen.2020.129512

M3 - Original Article

C2 - 31917998

SN - 0304-4165

VL - 1864

SP - 129512

JO - BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS

JF - BIOCHIMICA ET BIOPHYSICA ACTA-GENERAL SUBJECTS

IS - 4

ER -